常染色体显性遗传多囊肾

Autosomaldominantpolycystickidneydisease常染色体显性遗传多囊肾

来源：双语学影像；病例选自《MayoClinicBodyMRICaseReview》

47-year-oldwomanwithageneticdisorder

Fig2.1.1CoronalSSFSE

Fig2.1.2axialT1WIFSE

Fig2.1.3Axialfat-saturated2DSSFPimages

CoronalSSFSE(Figure2.1.1)andaxialT1-weightedFSE(Figure2.1.2)imagesdemonstrateinnumerablevariable-sizedcyststhroughouttheliverandkidneys.SomecystsshowhighT1-signalintensity.Axialfat-saturated2DSSFPimages(Figure2.1.3)showsimilarfindingsanddemonstratepatencyoftheintrahepaticIVC.

冠状位SSFSE序列和横断位T1WIFSE序列示肝脏及肾脏内布满大量大小不等的囊性病灶，部分囊于T1WI呈高信号。横断位脂肪抑制2DSSFP图像示下腔静脉肝内段通畅。

Diagnosis

Autosomaldominantpolycystickidneydisease

常染色体显性遗传多囊肾

ADPKDisarelatively